Occipito-thoracic Fusion in Incidental Dystropic Os Odontoideum in a patient suspected with Osteogenesis Imperfecta: A Case Report

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Acta Medica International,2015,2,1,172-173.
Published:January 2015
Type:Case Report

Occipito-thoracic Fusion in Incidental Dystropic Os Odontoideum in a patient suspected with Osteogenesis Imperfecta: A Case Report

Reyes Rechilda Rhea P1, Tangente Ronald P2, Soriano James A3, Lagapa Euvin Paul G4
1Neurological Surgery Resident Physician, Southern Philippines Integrated Neurological Surgery Training Program, Davao City, Philippines,
2Spine Surgery, Department of Orthopedics, Davao Doctors Hospital, Southern Philippines Integrated Neurological Surgery Training Program,Davao City, Philippines,

3Program Director, Department of Neurosurgery, Southern Philippines Integrated Neurological Surgery Training
Program, Davao City, Philippines,

4Training Offi cer, Department of Neurosurgery, Southern Philippines Integrated Neurological Surgery
Training Program, Davao City, Philippines

Abstract:

Introduction: Os odontoideum is a rare lesion of the axis. Described as an ossicle, consisting of smooth and separate caudal portions of the odontoid process wherein its etiology has remained controversial. Os odontoideum complicating a possible osteogenesis imperfecta has not been reported before in the literature. Methods: We report the case of a 14-yr male patient presented with progressive weakness of both lower and upper extremities after a head trauma 10 months prior to admission, which presented as transient quadreparesis. Results: Magnetic resonance imaging of cervical spine showing cervicomedullary junction compression. Patient underwent surgical intervention and 3 months post operation, patient was reported to have steady gait and muscle grading of 5/5 on all extremities. Conclusion: Surgical fi xation and fusion in patients with instability may prevent catastrophic neurologic insult after minor trauma in the future.

Postoperative lateral radiograph showing Occipito-thoracic fi xation and fusion using rods and screws